Primary micronodular bilateral adrenocortical hyperplasias (MiBAH) are rare challenging diseases. Important progress in understanding its pathophysiology and genetics occurred in the last two decades. We summarize those progress and recent data on investigation and therapy of MiBAH focusing on primary pigmented nodular adrenocortical disease (PPNAD).

中文翻译：

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最新的原发性小结节性双侧肾上腺皮质疾病。

原发性微结节性双侧肾上腺皮质增生（MiBAH）是罕见的具有挑战性的疾病。近二十年来，在了解其病理生理学和遗传学方面取得了重要进展。我们总结了有关MiBAH的研究和治疗方面的进展和最新数据，重点是原发性色素性结节性肾上腺皮质疾病（PPNAD）。