Since article was originally published online, some minor corrections which had been missed at the proof stage (due to OUP error) have since been updated: 1) In Fig, 5F, WT, and Smcr8-/- have been added into the labels, and also *, n.s. in the notes; 2) In Fig. 9C, GR has been amended to GP following a re-calculation, because the authors found that previous GR antibody recognizes non-specific autofluorescent proteins. The modifications did not change the conclusions and interpretation of the results.

中文翻译：

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在C9ALS / FTD小鼠模型中，Smcr8缺乏症破坏了依赖轴突运输的溶酶体功能，并促进了轴突肿胀和毒性增加。

自从文章最初在线发布以来，由于在更新阶段由于OUP错误而错过了一些小更正：1）在图5F，WT和Smcr8-/-中已添加到标签中，以及注释中的*，ns；2）在图9C中，由于作者发现先前的GR抗体识别非特异性自体荧光蛋白，因此在重新计算后将GR修改为GP。修改并没有改变结论和结果解释。