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Comparison of sporadic and familial behavioral variant frontotemporal dementia (FTD) in a North American cohort
Alzheimer's & Dementia ( IF 14.0 ) Pub Date : 2020-01-01 , DOI: 10.1002/alz.12046
Hilary W Heuer 1 , P Wang 1 , K Rascovsky 2 , A Wolf 1 , B Appleby 3 , J Bove 2 , Y Bordelon 4 , P Brannelly 5 , D E Brushaber 6 , C Caso 7 , G Coppola 4 , B Dickerson 8 , S Dickinson 9 , K Domoto-Reilly 7 , K Faber 10 , J Ferrall 11 , J Fields 6 , A Fishman 12 , J Fong 1 , T Foroud 10 , L K Forsberg 6 , D Gearhart 6 , B Ghazanfari 13 , N Ghoshal 14 , J Goldman 15 , J Graff-Radford 6 , N Graff-Radford 16 , I Grant 17 , M Grossman 2 , D Haley 16 , G-Y Hsiung 18 , E Huey 15 , D Irwin 2 , D Jones 6 , K Kantarci 6 , A Karydas 1 , D Kaufer 11 , D Kerwin 19 , D Knopman 6 , J Kornak 1 , J H Kramer 1 , R Kraft 6 , W K Kremers 6 , W Kukull 20 , I Litvan 21 , P Ljubenkov 1 , I R Mackenzie 18 , M Maldonado 4 , M Manoochehri 15 , S McGinnis 8 , E McKinley 22 , M F Mendez 4 , B L Miller 1 , C Onyike 12 , A Pantelyat 12 , R Pearlman 23 , L Petrucelli 16 , M Potter 10 , R Rademakers 16 , E M Ramos 4 , K P Rankin 1 , E D Roberson 22 , E Rogalski 17 , P Sengdy 18 , L Shaw 2 , J Syrjanen 6 , M C Tartaglia 13 , N Tatton 9 , J Taylor 1 , A Toga 24 , J Trojanowski 3 , S Weintraub 17 , B Wong 8 , Z Wszolek 16 , B F Boeve 6 , H J Rosen 1 , A L Boxer 1 ,
Affiliation  

Behavioral variant frontotemporal dementia (bvFTD) may present sporadically or due to an autosomal dominant mutation. Characterization of both forms will improve understanding of the generalizability of assessments and treatments.

中文翻译:

北美队列中散发性和家族性行为变异性额颞叶痴呆 (FTD) 的比较

行为变异额颞叶痴呆 (bvFTD) 可能偶发或由于常染色体显性突变而出现。两种形式的表征将提高对评估和治疗的普遍性的理解。
更新日期:2020-01-01
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